ornithine transcarbamoylase -->
ornithine carbamoyltransferase
medical dictionary

<enzyme>

<cell biology> An enzyme of the transferase class that catalyses the reaction of carbamoyl phosphate and l-ornithine to yield orthophosphate and l-citrulline. The enzyme occurs in the liver. The reaction is a part of the urea cycle. Genetic deficiency of the enzyme, an x-linked trait, impairs urea formation and produces hyperammonaemia.

Chemical name: Carbamoyl-phosphate:L-ornithine carbamoyltransferase

Registry number: EC 2.1.3.3

(12 Dec 1998)