|methylmalonyl-CoA mutase||medical dictionary|
<cell biology> An enzyme that catalyses the conversion of methylmalonyl-CoA to succinyl-CoA by transfer of the carbonyl group. It requires a cobamide coenzyme. A block in this enzymatic conversion leads to the metabolic disease, methylmalonic aciduria.
Chemical name: (R)-2-Methyl-3-oxopropanoyl-CoA CoA-carbonylmutase
Registry number: EC 220.127.116.11
(12 Dec 1998)
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